• Produktbild: Retinal Degenerations
  • Produktbild: Retinal Degenerations
Band 533

Retinal Degenerations Mechanisms and Experimental Therapy

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Beschreibung

Produktdetails

Einband

Taschenbuch

Erscheinungsdatum

11.02.2013

Herausgeber

Matthew M. LaVail + weitere

Verlag

Springer Us

Seitenzahl

467

Maße (L/B/H)

25.4/17.8/2.7 cm

Gewicht

909 g

Auflage

Softcover reprint of the original 1st ed. 2003

Sprache

Englisch

ISBN

978-1-4613-4909-9

Beschreibung

Produktdetails

Einband

Taschenbuch

Erscheinungsdatum

11.02.2013

Herausgeber

Verlag

Springer Us

Seitenzahl

467

Maße (L/B/H)

25.4/17.8/2.7 cm

Gewicht

909 g

Auflage

Softcover reprint of the original 1st ed. 2003

Sprache

Englisch

ISBN

978-1-4613-4909-9

Herstelleradresse

Springer-Verlag KG
Sachsenplatz 4-6
1201 Wien
AT

Email: GPSR Kontakt

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  • Produktbild: Retinal Degenerations
  • Produktbild: Retinal Degenerations
  • 1. IDENTIFICATION OF THE RP1 AND RP10 (IMPDH1) GENES CAUSING AUTOSOMAL DOMINANT RP.- 2. ON THE ROLE OF IMPDH1 IN RETINAL DEGENERATION.- 3. AN INTEGRATED GENETIC APPROACH TO IDENTIFY CANDIDATE GENES FOR HUMAN CHROMOSOME 6q-LINKED RETINAL DISORDERS.- 4. MOUSE GENETIC APPROACHES TO ACCESS PATHWAYS IMPORTANT IN RETINAL FUNCTION: A VALUABLE TOOL FOR THE ASSESSMENT OF NOVEL GENE THERAPIES.- 5. RETINAL DEGENERATIVE DISORDERS IN SOUTHERN AFRICA:A MOLECULAR GENETIC APPROACH.- 6. COMPARING ROD AND CONE FUNCTION WITH FUNDUS AUTOFLUORESCENCE IMAGES IN RETINITIS PIGMENTOSA.- 7. A MODIFIED PROTOCOL FOR THE ASSESSMENT OF VISUAL FUNCTION IN PATIENTS WITH RETINITIS PIGMENTOSA.- 8. PRENATAL HUMAN OCULAR DEGENERATION OCCURS IN LEBER’S CONGENITAL AMAUROSIS: (LCA 1 and 2).- 9. LEBER CONGENITAL AMAUROSIS — GENOTYPING REQUIRED FOR POSSIBLE INCLUSION IN A CLINICAL TRIAL.- 10. TREATMENT OF CYSTOID MACULAR EDEMA RELATED TO RETINITIS PIGMENTOSA WITH INTRAVITREAL TRIAMCINOLONE ACETONIDE: CASE REPORT.- 11. PROTEOMIC APPROACHES TO UNDERSTANDING AGE-RELATED MACULAR DEGENERATION.- 12. PROGRESSIVE PATHWAYS IN AGE-RELATED MACULAR DEGENERATION.- 13. TISSUE INHIBITOR OF METALLOPROTEINASES-3 AND SORSBY FUNDUS DYSTROPHY.- 14. INVESTIGATIONS OF RPE CELLS OF CHORIODAL NEOVASCULAR MEMBRANES FROM PATIENTS WITH AGE-RELATED MACULA DEGENERATION.- 15. RETINAL AND CHOROIDAL ALTERATIONS FOLLOWING PHOTODYNAMIC THERAPY.- 16. USHER SYNDROME: CORRELATION BETWEEN VISUAL FIELD SIZE AND MAXIMAL ERG RESPONSE B-WAVE AMPLITUDE.- 17. THE CELLULAR FUNCTION OF THE USHER GENE PRODUCT MYOSIN VIIA IS SPECIFIED BY ITS LIGANDS.- 18. MOUSE MODELS FOR USHER SYNDROME 1B.- 19. SCREEN FOR USHER SYNDROME 1B MUTATIONS IN THE OVINE MYOSIN VIIA GENE.- 20. PHOTORECEPTOR INTERSEGMENTAL TRANSPORT AND RETINAL DEGENERATION: A CONSERVED PATHWAY COMMON TO MOTILE AND SENSORY CILIA.- 21. INHERITED RETINAL DYSTROPHY IN MER KNOCKOUT MICE 165 Jacque L. Duncan.- 22. MOUSE MODELS OF HUMAN RETINAL DISEASE CAUSED BY EXPRESSION OF MUTANT RHODOPSIN.- 23. EVALUATION OF INNER RETINAL STRUCTURE IN THE AGED RCS RAT.- 24. THE INTACT XENOPUS LAE VIS EYE RUDIMENT: A QUASI-IN VIVO SYSTEM FOR THE STUDY OF RETINAL DEVELOPMENT AND DEGENERATIONS.- 25. STREPTOZOTOCIN-INDUCED DIABETES - A RAT MODEL TO STUDY INVOLVEMENT OF RETINAL CELL TYPES IN THE ONSET OF DIABETIC RETINOPATHY.- 26. A2E, A FLUOROPHORE OF RPE LIPOFUSCIN: CAN IT CAUSE RPE DEGENERATION?.- 27. BRIGHT LIGHT INDUCES RETINAL DEGENERATION BY A TRANSDUCIN-INDEPENDENT MECHANISM.- 28. DOES CONSTITUTIVE PHOSPHORYLATION PROTECT AGAINST PHOTORECEPTOR DEGENERATION IN RPE6S’MICE?.- 29. LIGHT-INDUCED PHOTORECEPTOR DAMAGE TRIGGERS DNA REPAIR: DIFFERENTIAL FATE OF RODS AND CONES.- 30. MITOCHONDRIAL DELETIONS IN NORMAL AND DEGENERATING RAT RETINA.- 31. QUANTITATIVE PCR ANALYSIS OF FosB mRNA EXPRESSION AFTER SHORT DURATION OXYGEN AND LIGHT STRESS.- 32. METABOLIC MODULATION OF VISUAL SENSITIVITY.- 33. MITOCHONDRIAL UNCOUPLING PROTEINS: REGULATORS OF RETINAL CELL DEATH.- 34. ENERGY DEPLETION HYPOTHESIS FOR RETINITIS PIGMENTOSA.- 35. FUNCTIONAL STUDIES OF AIPL1: POTENTIAL ROLE OF AIPL1 IN CELL CYCLE EXIT AND/OR DIFFERENTIATION OF PHOTORECEPTORS.- 36. PHOTORECEPTOR DEGENERATION IN PRO23HIS AND S334TER TRANSGENIC RATS.- 37. RETINAL DEGENERATION CAUSED BY MUTATIONS IN TULP1.- 38. TOWARDS UNDERSTANDING THE FUNCTION OF THE TUBBY GENE FAMILY IN THE RETINA.- 39. IDENTIFICATION OF DOWNSTREAM MECHANISMS INVOLVED IN PEDF’S ACTIVITY IN THE RETINA BY LARGE SCALE GENE EXPRESSION PROFILING.- 40. THE nob MUTATION DOES NOT PROTECT AGAINST LIGHT—INDUCED RETINAL DEGENERATION.- 41. THE PHAGOCYTOSIS OF OS IS MEDIATED BY THE PI3-KINASE LINKED TYROSINE KINASE RECEPTOR, MER, AND IS STIMULATED BY GAS6.- 42. ROLE OF avss5 INTEGRIN IN REGULATING PHAGOCYTOSIS BY THE RETINAL PIGMENT EPITHELIUM.- 43. COMPARATIVE STUDY OF CATHEPSIN D AND S IN RAT IPE AND RPE CELLS.- 44. ISOLATION AND CULTURE OF PRIMARY MOUSE RETINAL PIGMENTED EPITHELIAL CELLS.- 45. REGULATION OF THE VISUAL CYCLE: RETINOL DEHYDROGENASE AND RETINOL FLUORESCENCE MEASUREMENTS IN VERTEBRATE RETINA.- 46. MELATONIN ENHANCES RETINOIC ACID INDUCTION OF CONE ARRESTIN GENE EXPRESSION IN RETINOBLASTOMA CELLS.- 47. REGULATION OF RETINAL PHOSPHOINOSITIDE 3-KINASE ACTIVITY IN P85a-SUBUNIT KNOCKOUT MICE.- 48. PERIPHERIN/RDS IN SKATE RETINA.- 49. MAP PROTECTS PHOTORECEPTORS FROM N-METHYL-N-NITROSOUREA-INDUCED RETINAL DEGENERATION.- 50. NEUROPROTECTIVE EFFECT OF ESTROGEN UPON RETINAL NEURONS IN VITRO.- 51. TRANSGENIC RD MICE HARBORING AXOKINE GENE BY RPE65GENE PROMOTER DOES NOT RESCUE PHOTORECEPTOR DEGENERATION.- 52. MARROW STROMAL CELLS—MSCs: A SPECIES COMPARISON.- 53. GENE THERAPY FOR LEBER CONGENITAL AMAUROSIS.- 54. FUNCTIONAL AND STRUCTURAL EVALUATION AFTER AAV.RPE65 GENE TRANSFER IN THE CANINE MODEL OF LEBER’S CONGENITAL AMAUROSIS.- 55. ASSESSMENT OF rAAV-MEDIATED GENE THERAPY IN THE Rpe65
    MOUSE.- 56. MüLLER CELL TRANSDUCTION BY AAV2 IN NORMAL AND DEGENERATIVE RETINAS.- 57. VIRUS-MEDIATED SECRETION GENE THERAPY—A POTENTIAL TREATMENT FOR OCULAR NEOVASCULARIZATION.- ABOUT THE EDITORS.